Objective: To present a case of epithelial basement membrane dystrophy according to the IC3D Classification of corneal dystrophies Edition 2 and results after a phototherapeutic keratectomy.
Clinical case: A 61-year-old female with decreased visual acuity in both eyes, corneal opacities, subepithelial lines (map-like) in the central area of both corneas. Epithelial basement membrane dystrophy was diagnosed by confocal microscopy, and a phototherapeutic keratectomy was performed, achieving good corneal transparency, a normal confocal microscopy and visual recovery.
Conclusions: The IC3D Classification of corneal dystrophies IC3D Edition 2 facilitated the diagnosis of the case.The good morphological result, the significant visual acuity gain and the corneal regularity evidenced by Sirius® tomography demonstrate that phototherapeutic keratectomy is an effective treatment for epithelial basement membrane dystrophy.
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